Epidemiology
- Global Reports: BFIE cases have been reported worldwide.
- Prevalence and Incidence: Remain unknown.
Clinical Description
- Age of Onset: Seizures usually occur between 3 to 8 months of life.
- Seizure Characteristics:
- Clusters of 8-10 episodes a day.
- Each episode lasts 2-5 minutes over a few days.
- Typically focal but can become generalized.
Etiology
- Motor arrest, unresponsiveness, head and/or eye deviation to one side.
- Staring, fluttering of eyelids, grunting, cyanosis.
- Diffuse hypertonia and unilateral or bilateral clonic jerks of the limbs.
