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Flaccid Dysarthria (Lower Motor Neuron Lesion)
- Clinical Features:
- Lax open mouth
- Atonia
- Weakness
- Wasting
- Drooling
- Feeding difficulties
- Absent jaw, gag, and cough reflexes
- Causes:
- Dystrophia myotonica
- Prader-Willi Syndrome
- Myasthenia gravis
- Facio-scapulo-humeral dystrophy
- Congenital dysplasia of the brainstem (e.g., Moebius)
- Pontine gliomas
- Progressive motor neurone diseases (e.g., Fazio-Londe)
- Vascular lesions of the brainstem
- Posterior fossa tumour resection
- Clinical Features:
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Spastic Dysarthria (Upper Motor Neuron Lesion)
- Clinical Features:
- Release of brainstem reflexes
- Stiff jaw
- Difficulty opening mouth
- Brisk jaw jerk with clonus
- Small bunched tongue
- Rapid tongue movements are difficult
- Gag and cough reflexes present
- No wasting
- Causes:
- Cerebral palsy
- Degenerative brain diseases (e.g., Batten disease, Metachromatic leukodystrophy)
- Acquired traumatic brain injury
- Clinical Features:
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Dysarthria Associated with Cerebral Palsy
- Clinical Features:
- Unwanted movements interfering with normal articulation
- Retention of obligatory feeding reflexes
- Gag and cough reflex retained
- Causes:
- Kernicterus
- Hypoxic-ischemic brain injury
- Degenerative diseases of the basal ganglia
- Clinical Features:
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Ataxic Dysarthria (Cerebellum)
- Clinical Features:
- Gag and cough reflex retained
- Disrupted rhythm and volume control
- Features of verbal dyspraxia
- Slow development of speech articulation
- Causes:
- Congenital abnormalities of the cerebellum
- Posterior fossa resections
- Syndromic examples (e.g., Joubert syndrome)
- Post-acquired cerebellar disorders
- Clinical Features:
Source: Aicardi, J., Bax, M., Ogier, H., Polani, P., & Vizioli, R. (Eds.). (2018). Aicardi's Diseases of the Nervous System in Childhood (4th ed.). Mac Keith Press.